We offer a complete range of Foods for Special Medical Purposes as carbohydrate substitutes suitable for inclusion in the dietary management of patients requiring a ketogenic diet, at the forefront of nutrition and, at the same time, capable of addressing the diverse needs of patients in an easy manner.
These Foods for Special Medical Purposes provide patients with the opportunity to choose, allowing them to adhere to their preferred dietary management through the implementation of the ketogenic diet without sacrificing traditional eating habits.
An important aspect in implementing the ketogenic diet is the issue of food palatability, especially compared to a typical Mediterranean diet. This problem becomes even more apparent in individuals who must maintain such a diet for many years or for their entire life, as in the dietary management of Glucose Transporter Type 1 Deficiency Syndrome (Glut1 DS).
Epilepsy is a disorder of the central nervous system characterized by the persistent occurrence of sudden seizures, often multiple times a day, which strike without warning and manifest with involuntary, abrupt, and uncontrolled muscle movements, sometimes accompanied by loss of consciousness, leading to overall deterioration.
Congenital Metabolic Diseases (CMD) constitute a category of genetic diseases caused by altered functioning of a specific metabolic pathway. Most individuals affected by these inherited disorders have a defective gene that causes a deficiency of enzymes. There are hundreds of different inherited metabolic diseases, with diverse symptoms, prognosis, and therapies.
Glycogen storage diseases (GSD) type III, V, and VII share a part of the clinical picture consisting of progressive intolerance to exertion, muscle pains, and cramps with deterioration of muscle structure, which increasingly loses its functional capabilities. The underlying cause of this muscle damage is that the enzymatic defect in these diseases prevents the correct use of carbohydrates to produce energy because the normal activity of glycogenolysis (GSD III and GSD V) or glycolysis (GSD VII) is blocked.
Glucose transporter type 1 deficiency syndrome (Glut1 deficiency syndrome or Glut1-DS) is a rare genetic disease that compromises the normal transit of glucose from the blood to the brain, causing the absence or a severe reduction of glucose in the brain, with extremely serious brain consequences. GLUT1 deficiency syndrome is a genetically determined neurological disorder caused by inadequate glucose transport into the brain.
Pyruvate dehydrogenase is an enzyme complex that allows the transformation of the food we eat into the energy our cells need to function. Deficiency of this enzyme complex results in the accumulation of the protein pyruvate and its conversion into lactic acid or decreased energy production, with damage primarily affecting the brain, which requires a significant amount of energy to function and grow.”